Archive of Old Cases
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- Archive of Old Cases
- 2001
Case No : 210 Date 2001-11-03
- Courtesy of Jin Mo Goo, M.D, Jung-Gi Im, M.D. / Seoul National University Hospital, Seoul, Korea
- Age/Sex 25 / M
- Chief ComplaintAcute chest pain
Discussion
Diagnosis With Brief Discussion
- Diagnosis
- Aortic Dissection in a Patient with Marfan's Syndrome
- Radiologic Findings
- Posteroanterior chest radiography shows scoliosis of the thoracic spine. Transverse contrast-enhanced CT scan and CT angiography reformatted to oblique sagittal plane show marked enlargement of the aortic root and an intimal flap in the ascending aorta.
- Brief Review
- Marfan’s syndrome is an autosomal dominant disorder with a variable expression, involving particularly the eyes (myopia, ectopia lentis), aorta and heart (aortic aneurysm, aortic dissection, aortic regurgitation, mitral valve disease), and musculoskeletal system (relatively long limbs in relationship to the trunk, arachnodactyly, pectus deformities, kyphoscoliosis, and joint laxity).
The chief respiratory abnormalities in Marfan’s syndrome are pneumothorax, bullae, cysts, and emphysema. A particularly striking manifestation of Marfan’s syndrome is bullae occurring in young patients. - References
- 1. Armstrong P, Wilson AG, Dee P, Hansell DM. Imaging of diseases of the chest. 3rd ed. Mosby, London, 2000;767-768
2. Wood JR, Bellamy D, Child AH, et al. Pulmonary disease in patients with Marfan syndrome. Thorax 1984;39:780-784 - Keywords
- Vascular, Chest wall, Vascular, Congenital,
No. of Applicants : 27
- ▶ Correct Answer : 12/27, 44.4%
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- - 嫄닿뎅
- - 嫄댁
- - 寃쏀ъ猷 怨
- - 怨
- - 怨
- - 怨
- - 源吏
- -
- -
- - 遺 理以
- -
- - 源
- ▶ Semi-Correct Answer : 2/27, 7.4%
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- - 遺 理湲곕났
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